ҽѧÉϵIJ¡ÃûÕæµÄÊÇǧÆæ°Ù¹Ö£¬Õâ¸ö×ÛºÏÕ÷£¬ÄǸöÏÖÏóµÄ£¬Ò²²»×ãΪÆ棬µ«ÎÒ½ñÌì·ÖÏíµÄPOEMS×ÛºÏÕ÷²»ÖªµÀÄãÌý¹ýû£¿ÎÒÒ²ÊǵÚÒ»´ÎÌý˵¡£Èç¹ûûÓÐÌý¹ý£¬½ñÌì¾Í¿ÆÆÕһϰɡ£
»¼Õߣ¬Å®£¬58Ë꣬ÓÚ°ëÔÂÇ°ÎÞÃ÷ÏÔÓÕÒò½¥Æð¸¹ÕÍ£¬³öÏÖÅűãÀ§ÄÑ£¬Ê®ÓàÌìδ½â´ó±ã£¬Å¼ÓÐÆêÖÜÒþÍ´£¬ÎÞ·¢ÈÈÄò»ÆðþÑ÷£¬ÔÚ¼Ò×Ô·þÏ㵤ÇåÖÎÁÆ£¬¸¹ÕÍ믧½â¶ø¾ÍÕÒÔÂýÐԽ᳦Ñ×ÊÕÖÎÈëÔº¡£¼ÈÍùÊ·£º»¼Õß2017Äê5ÔÂÔÚÎ人ÊеÚÒ»Ò½Ôº¼°ÐºÍÒ½ÔºÕï¶Ï“POEMS×ÛºÏÕ÷”£¬¾ßÌå·þÒ©²»Ï꣬Ìå¸ñ¼ì²é£ºT£º37.2¡æ£¬P£º80´Î/·Ö£¬R£º20´Î/·Ö£¬BP£º155/85 mmHg£¬Æ¤·ôÎÞ»ÆȾ£¬Ã沿¿É¼ûÉ«ËسÁ×Å£¬Ë«ÏÂÖ«¿É¼ûÉ¢ÔÚÀ£Àü°³Â¾ÉÐÔÓúºÏ°ÌºÛ¡£¿É¼ûÖÜΧÉñ¾²¡±ä£¬×ÔÖ÷Éñ¾¹¦ÄÜÕÏ°£¬È縹ÕͱãÃصÈΪ¸Ã²¡Ö¢×´¡£
¼²²¡Ç§Ææ°Ù¹Ö£¬±¾À´Ó¦¸ÃÊǼû¹Ö²»¹Ö£¬Òª²»ÊÇѪ³£¹æºÍÄýѪ¹¦ÄÜÒì³£Ò²²»»áÒýÆðÎÒµÄ×¢Òâ¡£¼ÇµÃµ±Ê±»¤Ê¿ËÍѪ¹ýÀ´µÄʱºòÊDZ¼ÅÜ׏ýÀ´µÄ£¬ËµÕâ¸ö²¡È˱ȽÏÌØÊ⣬Ҫµ±°àÈËÔ±Á¢¼´¼ì²â£¬µ±Ê±Öµ°àµÄºúÒ½ÉúÁ¢¼´½«Ñª³£¹æÉÏ»ú¼ì²â£¬µ«¼ì²â½á¹ûÈ´ÊÇÕâÑùµÄ£º
Ò»¿ªÊ¼ÎÒÒÔΪÊÇÀäÄý¼¯ÏÖÏó£¬×¼±¸ÎÂÓýÊÔÊԲ鿴£¬½á¹ûÎÂÓýÖ®ºó¸ù±¾Ã»ÓÐÈκθı䣬³öÓÚºÃÆæÎҵ㿪»¼Õß²¡Àýϵͳ£¬²ÅÖªµÀ»¼ÕßÔÚÍâԺȷÕïΪ“POEMS×ÛºÏÕ÷”£¬µ«Õâ¸ö“POEMS×ÛºÏÕ÷”ÊǸöʲô¹í£¬ÎÒÒÀÈ»²»Öª£¬ÓÚÊÇÏëÆðÁ˶ÈÄï¡£
°Ù¶ÈһϓPOEMS×ÛºÏÕ÷”ÊÇÒ»ÖÖ²¡ÒòºÍ·¢²¡»úÖƲ»ÇåµÄÉÙ¼ûµÄ¶àϵͳ¼²²¡£¬Ö÷Òª±íÏÖΪ¶à·¢ÐÔÉñ¾²¡±ä(polyneuropathy£¬P)¡¢ÔàÆ÷Ö×´ó(organomegaly£¬O)¡¢ÄÚ·ÖÃÚ²¡±ä(endocrinopathy£¬E)¡¢µ¥¿Ë¡γÇòµ°°×²¡(monoclonal gammopathy£¬M£¬Ò²½ÐM-µ°°×)ºÍƤ·ô¸Ä±ä(skin changes£¬S)¡£±¾²¡ÓÚ1956ÄêÊ×ÏÈÓÉCrowÃèÊö£¬1968ÄêËæºóÓÉFukaseÃèÊö¡£NakanishiµÈ½«Æä³ÆΪCrow-Fukase×ÛºÏÕ÷¡£TakatsukiÊ×ÏÈÈ·Èϲ¢È«ÃæÃèÊö±¾²¡£¬Òò´ËÒ²ÓÐÈ˳ÆΪTakatsuki×ÛºÏÕ÷¡£POEMSÔÀ´Éæ¼°µ½Õâô¶àϵͳµÄ²¡±ä£¬¸úÄǸöSLEºÍMDSÓеÄһƴ¡£
û°ì·¨Ö»ÄÜÈû¼ÕßÇ××ÔÀ´ÌË¿ÆÊÒ£¬ÎÒÃÇÏÖ³¡³éѪ£¬¼´¿Ì²â¶¨£¬Õ÷µÃ²¡ÈËͬÒ⣬»¼Õß˳Àû²ÉÑù£¬Á¢¼´ÉÏ»ú¼ì²â¡£